why do i smell like pancake syrup

Both parents must carry a mutation of the gene associated with MSUD to pass the disease onto their child. There isnt enough evidence backing up those claims yet & plus pancakes dont get fluffly on their own do they?. But it isn't a chronic condition. The seeds are used in cooking, to make medicine, or to hide the taste of other medicine. Your pumpkin spice beverages, and granola bars, and candies, and candles, are made with a mix of molecules that may include sotolon, too. But being tired all the time is certainly a symptom of diabetes. Maple Syrup May Protect Brain From Alzheimers And Other Neurodegenerative Disease, Maple Syrup Extract Could Make Antibiotics More Effective Against Bacteria, 2023 Medical Daily Inc. All rights reserved. However, you don't find anything. What does it mean when your sweat smells like maple syrup? He obtained his master and Ph.D. degrees from the University of So Paulo, Brazil, and worked as a postdoctoral researcher at the Karolinska Institute, Sweden. Fenugreek contains an extremely potent aromatic compound called solotone. Gus: "We got stuck in traffic". My first thought is that your boyfriend might have maple syrup urine disease (unrelated to diabetes) or diabetic ketoacidosis, which is serious diabetes complication where the body produces. 21st ed. That's because a healthy liver can produce the proper enzymes needed to break down the amino acids that accrue in the body and cause problems. In older children, signs of intermediate, intermittent, and thiamine-responsive MSUD usually develop before age seven. which benefit does a community experience when its members have a high level of health literacy? In color and flavor, they range from light to dark, with the grade's name describing both coloring and flavor intensity. URAC's accreditation program is an independent audit to verify that A.D.A.M. After they are topped, you can also add the smells of melted butter and syrup to the mix. With a leakage, there is a shortage of coolant circulating throughout. This can be a symptom of a health issue. Driving your car with low coolant can damage your car, mainly because it may increase your chances of engine overheating. "We use them a lot for fleshiness in strawberry or coffee. This well-rounded fragrance is composed of notes of freshly baked cake, hot maple syrup, sweet cream butter, and rich buttermilk, all sitting on a wonderful base note of a nice lingering vanilla. For additional information visit Linking to and Using Content from MedlinePlus. And theres even a connection to funny-smelling pee: Sufferers of a rare genetic disorder called maple syrup urine disease cant process certain amino acids properly, leading, through a series of chemical steps, to sotolonand its distinctive odorin their excretions. Pancakes have a warm, lightly sweet, breadlike smell. It is caused by a defect in 1 of 3 genes. This site complies with the HONcode standard for trustworthy health information: verify here. Possible causes of this especially foul-smelling puppy breath include dental and oral hygiene issues, like severe periodontal disease in their gums (which can lead to infection and tooth loss) and even more serious issues, like a tooth abscess or oral tumor. You Might Be a Supertaster (and Not a Picky Eater), According to a Nutritionist, 8 Tips for Making the Best French Toast Ever, 93 Christmas Baking Recipes for Festive Cookies, Bars, and Bites, Honey Isn't Vegan, But These 6 Alternatives Most Certainly Are. When it comes to stuff smelling like food nothing beats the way silicone caulking smells like salt and vinegar chips. what makes muscle tissue different from other tissues? We use cookies on our website to give you the most relevant experience by remembering your preferences and repeat visits. You probably dont have maple syrup urine disease because its a rare inherited disorder that affects an estimated 1 in 185,000 infants worldwide, according to the National Institutes of Health. MSUD is an inherited disorder that results from the bodys inability to properly process certain protein building blocks called amino acids. It does not store any personal data. You also have the option to opt-out of these cookies. After 25 years working her way up through the ranks of the company and training in tasting and chemistry, shes now in charge of formulating savory, sweet, and beverage flavors for brands youve definitely heard of, but which shes not allowed to name. Its bitter!" Either way, use a delicate hand so as not to deflate the whites or whipped cream. But even an experienced Indian chef has trouble describing exactly what methi tastes like on its own. They eventually spill over into the urine, giving it a maple syrup-like smell. ", The molecule responsible for both methi and the Manhattan Maple Whodunit is sotolon (sometimes spelled with an "e" at the end"sotolone"), which is present in fenugreek in large quantities and pops up in all sorts of other unexpected places. Some of the initial symptoms of classic MSUD include irregular sleep patterns, lethargy, irritability, weight loss, poor appetite, and a distinctive maple sugar odor in earwax, sweat, and urine (which gives the disorder its name). CDC Adjusts COVID-19 Vaccination Requirement For Travelers Heading To US, AstraZeneca's AZD3152 Combats All COVID-19 Variants, Including Arcturus, Single Endoscopic Treatment Could Eliminate Need For Insulin In Type 2 Diabetes Patients, Long Midday Naps May Increase Risk Of Obesity, High BP, And Metabolic Syndrome. If he is taking a lot of whey protein powder, he's getting a lot of branched-chain amino acids, and they have an odor of maple syrup. In the most severe form, MSUD can damage the brain during times of physical stress (such as infection, fever, or not eating for a long time). But TJ's 12-ounce "Organic Maple Syrup" for $7.99 is one with deep charms and is available in a smaller glass package. Either that, or maybe your neighbour is moving and doesn't want to chuck out the pancake mix. Also reviewed by David Zieve, MD, MHA, Medical Director, Brenda Conaway, Editorial Director, and the A.D.A.M. If the smell is coming from your dog's fur (rather than her breath), it might be caused by a yeast infection. The excess sweating brought on by these hormonal fluctuations doesnt help either- thereby fermenting/prolonging the scent longingly as it were. that allows smells from adjoining dwellings to come into your home. This website uses cookies to improve your experience while you navigate through the website. This disease can be life threatening if untreated. If you're battling this condition, your urine will smell like maple syrup . The culprit leans more towards pure organic maple syrup that youve over consumed lately. Kare Raisu (Homemade Japanese Curry Rice) Recipe, The Story of Carolina Gold, the Best Rice You've Never Tasted, Kanuchi (Cherokee Pureed Nut Soup) Recipe, The History of Popcorn: How One Grain Became a Staple Snack, Shining a Light on Diwali Treats: An Opinionated Guide, The Best Cookbooks of 2022, According to Our Editors, Where to Buy Indian Ingredients in New York City, Adam Kuban Deep-Dishes on Slice, Margot's, and His Pizza Dreams, An Introduction to the Maillard Reaction: The Science of Browning, Aroma, and Flavor, How to Stock an Indian Pantry: Spices, Dals, and More Essential Ingredients, Ghosts of Thanksgivings Past: Our Highest Highs and Lowest Lows. Car Smells Sweet Like Syrup: What Is It and What Do I Do. Best Thick Texture: Mrs. Butterworth's Original Pancake Syrup. Best Pancake Syrup at a Glance: Best Overall: Pearl Milling Company Country Rich Homestyle Syrup. That being said, more frequent or dry mouth subjecting individuals are prone to developing a pancake flavoured odor as dehydration is a major contributing factor (cue lesson#2) producing excess ketones while burning fat stores for energy. Your first thought may be to check your backseat for any leftovers you left in the car or if you've spilled a sugary snack in the car. follows rigorous standards of quality and accountability. Dialysis through your belly or a vein can be done to reduce the level of abnormal substances in your blood. Irreversible harm can occur when an engine . My boyfriend all the sudden started smelling very strongly of maple syrup. The name comes from maple syrup urine disease (MSUD), making it difficult for the body to break down some proteins. For infants, the diet includes a formula with low levels of the amino acids leucine, isoleucine, and valine. Even in the mildest form, repeated periods of physical stress can cause intellectualdisability and high levels of leucine to build up. These cookies track visitors across websites and collect information to provide customized ads. Your first thought may be to check your backseat for any leftovers you left in the car or if you've spilled a sugary snack in the car. It can be used in drinks like mojitos. 4/21/2023. So, before you start worrying about your blood sugar, rest assured that your odor is MOST LIKELY caused by your protein intake. If your house smells like maple syrup, it could indicate there's a leakage in your air conditioning unit's coils. Does natures plus red yeast rice contain citrinin? It should be celebrated, and, best of all, it doesn't have to cost all that much. But what if you woke up one morning and realized that you didnt have to go out for breakfast because you were the pancake? What should waffles smell like when they are done cooking? Late on the night of October 28, 2005, and early into the next morning, New York Citys 311 service hotline was flooded with calls reporting a strange odor wafting across Manhattan. What they do remember is that their dad always had time to make their Sundays extra special. Stop all forms of sugar and alcohol and obtain high dose thiamine from the health food store. The coolant moves through other parts, including the. "That was my first memory of methi. You can find out more about our use, change your default settings, and withdraw your consent at any time with effect for the future by visiting Cookies Settings, which can also be found in the footer of the site. Whats the best way to make homemade waffles? A stunt from the Eggo people? To make maple syrup, artisans tap maple trees that can grow more than five stories tall, extract sap, and then boil it down. The cookie is used to store the user consent for the cookies in the category "Performance". It can be used to glaze grilled fish. Try These 13 Alcohol-Free Spirits, 21 Trader Joe's Pumpkin Productsand Other Fall Foods You Need to Try, Hate Bitter Foods? URL of this page: //medlineplus.gov/ency/article/000373.htm. People with this condition cannot break down the amino acids leucine, isoleucine, and valine. Ahem. Every Sunday morning, his dad would get up early to make the family pancakes and homemade syrup. This condition is also called BCKD deficiency; branched-chain alpha-keto acid dehydrogenase deficiency; branched-chain ketoaciduria; and ketoacidemia. One I really like is in 100 Clues. With a maple syrup like this, think beyond the pancake. Home Recipes Dishes & Beverages Condiments. As soon as you catch this scent in your car, be sure to take your vehicle to the experts here at Monkey Wrenches. People with this condition cannot break down the amino acids leucine, isoleucine, and valine. And again a year after that. Not only does cooking them to golden-brown impart a better, crisp texture, it adds flavor. Linking to and Using Content from MedlinePlus, U.S. Department of Health and Human Services. Performance cookies are used to understand and analyze the key performance indexes of the website which helps in delivering a better user experience for the visitors. Best Sweet Flavor: Michele's Gourmet Maple Creme Syrup. Brentwood, CA 94513 (925) 634-4145, Imagine getting into your car and smelling an overwhelmingly sweet smell, similar to pancake syrup. Symptoms of classic MSUD appear in newborns within 48 hours of birth. Copyright 1997-2023, A.D.A.M., Inc. Any duplication or distribution of the information contained herein is strictly prohibited without authorization. Merritt JL, Gallagher RC. By Matt Stieb. I'm pretty sure it's not supposed to smell like maple syrup, or much of anything for that matter. Epilespy can make one smell odd smells. As you probably already know, mold is a . Printer Friendly | Permalink | | Top. Beyond method and origins, maple syrup differs from pancake syrup in taste, texture, and price point. Coolant acts as a temperature stabilizer and transferer to provide heat to your cabin heating and defrosting systems. Sotolons texture also makes it useful for the elusive component of flavor called mouthfeel. We recommend our users to update the browser. It causes an inability for the body to break down the amino acids valine, leucine and isoleucine. 4 Why does my 2 year olds pee smell sweet? What happens after 2 weeks of not smoking? Directions. Pancake syrup is cheaper because it is a more scalable, industrial product. Was it terrorism? And some of the other natural sources of the chemical do the same. Check if you have any of the other symptoms on the . This disorder may be fatal if left untreated. Maple syrup urine disease (MSUD) is a metabolic disorder that is genetically inherited 2. Illuminate Your Goodness: Inspiring I am a Good Person Quotes. The urine of people with this condition can smell like maple syrup. This results in a batter thats light and ethereal, but not overly rich. Be sure to consult a doctor if you have any of these symptoms. It's such a subtle line. Sotolon is a lactone, which has a very specific definition related to molecular structure thats way too complicated to talk about here. In this article (just kidding no in this article here), well dive into some possible reasons for your sweet scent. Individuals with the disease must also remain on a protein-restrictive diet that limits the amount of branched-chain amino acids they take in. All four types of MSUD have symptoms including: Urine, sweat, or earwax that smells like maple syrup or burnt sugar. Although it's called maple syrup urine disease, it can also make your sweat smell like maple syrup. Cooking pancakes at the wrong temp. We're at a lost to know where it began, and the smell seems to be getting stronger.". Yeast infections can cause a smell that's either sickly-sweet or sour. to the mix. Medical Daily is for informational purposes and should not be considered medical advice, diagnosis or treatment recommendation. This process has ancient rootsthe earliest Western maple syrup makers in Canada and the American Northeast learned from indigenous people, who had been using the sap of maple trees for a long time. "Ive used it in banana, pumpkin, elderflower, strawberry, and peach flavors," says Kim Juelg, a principal flavorist for Givaudan, the worlds largest maker of flavorings and scents. Rather, the sugar and thick, sticky body come from other sweeteners (often corn syrup) and added colorings (rather than development through the cooking process). Have you been making pancakes in your sleep or did Aunt Jemima personally spill her contents all over you last night? It can be used to glaze grilled fish. Gallagher RC, Enns GM, Cowan TM, Mendelsohn B, Packman S. Aminoacidemias and organic acidemias. The cookie is used to store the user consent for the cookies in the category "Other. With an important role in both curries and fake caramel, sotolon atomically bridges the divide between sweet and savory. The coolant moves through other parts, including the engine, hoses, radiator, and heater core. People with heightened levels of androsterone (a naturally occurring steroid hormone) can emit a maple syrup-like odor in their sweat (gross but true). When i first bought it I know it didn't smell of anything, it's just been for the last month maybe which I found weird. In fact, Trader Joe's offers a great selection of maple syrups that become even more affordable (per ounce) as you buy bigger bottles. By clicking Accept All Cookies, you agree to the storing of cookies on your device to enhance site navigation, analyze site usage, and assist in our marketing efforts. Remove from the heat; stir in maple flavoring. Mahendro grew up in Punjab, in northern India, where methi seeds often go into pickles. This condition is one type of amino acid disorder. Why do I smell syrup in my house? So the next time youre wandering the streets and get an overwhelming whiff of maple syrup (assuming youre not in Vermont in early spring), look for a spice factory or an Indian restaurantno need to call the police. Certain infections have been known to cause unusual body odors. This causes a build-up of harmful levels of these substances in the blood. When it comes to your vehicle, a consistent sweet smell in your vehicle can be a dangerous sign of a car issue. Necessary cookies are absolutely essential for the website to function properly. In a small saucepan, combine the sugars and water. These cookies will be stored in your browser only with your consent. Want to know more about maple syrup urine disease and its symptoms? Well Duh! Fenugreek "Grade A: Dark Color & Robust Flavor," when made well, unfolds with deeper, more enticing caramelized flavors. Maple syrup urine disease is a genetic disorder where a person cannot process certain proteins. Stuff youre trying to give a fuller mouthfeel without being sweet." Maple syrup urine disease (MSUD) is a disorder in which the body cannot break down certain parts of proteins. Is spring water better than purified drinking water? Excuse me, miss/ sir / non-binary pal (no /). You should know: The answer above provides general health information that is not intended to replace medical advice or treatment recommendations from a qualified healthcare professional. 6th ed. See more Reply Save Like G George6488 Sotolons "heavy" stickiness and slow evaporation is how it was able to blow across the Hudson, but the reason so many people noticed the maple smell is that its especially potent. How long should you meditate as a Buddhist? Do you mysteriously smell maple syrup everywhere? Musty-smelling urine is often the result of liver disease or liver failure. Conditions such as hyperhidrosis (excessive sweating), diabetes , and liver failure are commonly associated with sweet-smelling scents that vaguely resemble pancakes. There are five grades of maple syrup. The blue waffles infection makes the patients feel severe pain along with the feelings of severe itching and burning. This cookie is set by GDPR Cookie Consent plugin. Swaiman's Pediatric Neurology: Principles and Practice. are topped, you can also add the smells of melted butter and syrup Should that fail, call a local mechanical contractor. By continuing to use this site you consent to the use of cookies on your device as described in our cookie policy unless you have disabled them. Are all medicare advantage plans the same? Call 911 for all medical emergencies. Additionally, our techs can also assess any damage that has been created within the system. Puberty changes a lot in our bodies, including the way we smell. The urine of people with this condition can smell like maple syrup. Analytical cookies are used to understand how visitors interact with the website. Other uncategorized cookies are those that are being analyzed and have not been classified into a category as yet. is also a founding member of Hi-Ethics. Lets wrap this up by clarifying- old sweat stands strong and usually makes a person smell like a foot-ball field. Certain infections have been known to cause unusual body odors. Nelson Textbook of Pediatrics. This disorder may be fatal if left untreated. Why do parts of Vegas smell like pancakes/syrup occasionally. To use the sharing features on this page, please enable JavaScript. One time she said, bite this. I chewed on some and they were so bitter I never wanted to taste them again!" When that heater core gets a leak (usually pinhole size), the coolant make the sweet smell like syrup. If Your Dog is Suffering From Yeast Infection or Other Allergies. Remember, the pictures of blue waffles are unpleasant. Philadelphia, PA: Elsevier; 2020:chap 103. Rodrigo Barros is an endocrinologist and specializes in obesity, diabetes mellitus, and insulin resistance. It is possible for children to develop less severe forms of the disorder. Lorrie McCurdy, Farmington, New Mexico, Pancake Syrup Recipe photo by Taste of Home. But opting out of some of these cookies may affect your browsing experience. And fake maple syrup isn't necessarily worse . Copy. Not always. Then-hit TV show 30 Rock even made a joke about the mysterious smell. Pancakes. 1. For the last few days I keep smelling pancake syrup and I havent - Answered by a verified Health Professional We use cookies to give you the best possible experience on our website. But TJ's 12-ounce "Organic Maple Syrup" for $7.99 is one with deep charms and is available in a smaller glass package. These cookies ensure basic functionalities and security features of the website, anonymously. 2 tablespoons: 102 calories, 0 fat (0 saturated fat), 0 cholesterol, 4mg sodium, 26g carbohydrate (26g sugars, 0 fiber), 0 protein. Body and urine odor It is believed that excess consumption of fenugreek can make your sweat and urine smell pungent, just as eating asparagus changes the colour of your urine. WHAT IS MSUD? In Case Your Dog Has Chewed the California Cudweed. One of the lovely side effects of fenugreek is your sweat and baby smells like maple syrup. If you enjoy pancakes with all those toppings even after finding out what causes that annoying ol pancake stench -perhaps consider choosing light syrup unless its truly worth losing your significant others company because IT lingers (eyes rolling) Give your loved ones or co-workers some respite from the Pancake-Patient Syndrome -(not official medical terminology). Symptoms of classic MSUD appear in newborns within 48 hours of birth. Genetic counseling is suggested for people who want to have children and who have a family history of maple syrup urine disease. They should smell toasty and nutty, and should definitely have a little color on them. Created for people with ongoing healthcare needs but benefits everyone. Streptococcus anginosus may be beta-hemolytic or nonhemolytic. Imagine getting into your car and smelling an overwhelmingly sweet smell, similar to pancake syrup. Your body expels these molecules alongside regular sweating after consumption- which could result in being asked if someone can take a swipe at your arm with their tongue (seriously though, cut that mess out). At breakfast time, it tends to drizzle out of the bottle slowly, glopping and hanging. 4. Avery's Diseases of the Newborn. Inborn errors of carbohydrate, ammonia, amino acid, and organic acid metabolism. We hate to break it to you, but Aunt Jemima and Mrs. Butterworth bothhave imposter syndrome. So give us a call or stop by our shop today! People with this condition must remain on a diet low in these amino acids for life. Liver transplantation has been used to treat individuals with classic MSUD, according to the National Organization for Rare Diseases. Such feelings must make someone cant live a normal life just like normal people. Often called by its Hindi name, methi, fenugreeks seeds and leaves can be found in stews and spice mixes throughout most of the varied regional cuisines of India and Pakistan. Instead, I think that it's probably a result of a high amount of protein that your boyfriend is eating. He couldn't smell it because he was use to it. A.D.A.M., Inc. is accredited by URAC, for Health Content Provider (www.urac.org). Coolant acts as a temperature stabilizer and transferer to provide heat to your cabin heating and defrosting systems. Even with dietary treatment, stressful situations and illness can still cause high levels of certain amino acids. Some antibiotics belonging to categories like Penicillin types may contribute too however its occurrence is remain debatable since smells are subjective as well. One illness related to producing sweet smelling skin secretions is called Maple Syrup Urine Disease. People go through the trouble of drawing and boiling sap from tall, cold trees for a reason: Pure maple syrup can be a beautiful thing. The name comes from maple syrup urine disease (MSUD), making it difficult for the body to break down some proteins. "The oiliness of lactones just lays there and sticks on your tongue," Juelg says. 6. Urine may smell sweet if it contains extra glucose, which is a type of sugar. A licensed physician should be consulted for diagnosis and treatment of any and all medical conditions. It is possible for children to develop less severe forms of the disorder. In: Swaiman KF, Ashwal S, Ferriero DM, et al, eds. Advertisement cookies are used to provide visitors with relevant ads and marketing campaigns. After they If you continue to use this site we will assume that you are happy with it. Another kind is called intermediate MSUD, which affects babies with a higher level of enzyme activity than classic MSUD, and theres also a mild version of the disease called intermittent MSUD. We've looked in the attic, checked for bees, but there's nothing. Learn how we can help Refrigerate leftovers. This leads to a buildup of these chemicals in the blood. Coolant, also known to be a mixture of antifreeze and water, has a critical job when it comes to keeping your vehicle cooled. If you notice that air smells like maple syrup, it could be that there is mold in your house. My Dog's Fur Smells Like Maple Syrup! Symptoms of the disease range depending on the type. 's editorial policy editorial process and privacy policy. Review provided by VeriMed Healthcare Network. It would be wise to have your fasting blood glucose checked, especially if you have a family history of diabetes. When you visit the site, Dotdash Meredith and its partners may store or retrieve information on your browser, mostly in the form of cookies. You've probably tasted the answer at home, in diners, and at pancake houses. Maple syrup urine disease (MSUD) is a disorder in which the body cannot break down certain parts of proteins. It "tastes" kind of thick, if that makes any sense. How does it feel to have blue waffles disease? It is caused by a defect in 1 of 3 genes. If you catch yourself sniffing syrup, there's a strong likelihood that you've got a coolant leak. Inside your car is a heater / defroster that has antifreeze coolant circulating throughout. Some of the initial symptoms of classic MSUD include irregular sleep patterns, lethargy, irritability, weight loss, poor appetite, and a distinctive maple sugar odor in earwax, sweat, and urine (which gives the disorder its name). Can confirm, the art sleeves have a certain smell similar to lovage to them. Why do I smell like maple syrup when I sweat? It is responsible for regulating your engine's temperature to avoid overheating. In a small saucepan, combine the sugars and water. Until it popped up again one day in March 2006. Pancakes have a warm, lightly sweet, breadlike smell. Alcohol gets metabolized through the liver doesnt usually emit sweet aromas during these processes! Urine can reveal a lot about someones health. Thats right; you smell like syrup. If your house smells like maple syrup, it could indicate theres a leakage in your air conditioning units coils. But for flavor purposes, lactones tend to be oily, and dont dissolve well in water. Driving your car with low coolant can damage your car, mainly because it may increase your chances of engine overheating. However, you may visit "Cookie Settings" to provide a controlled consent. When you use maple syrup, you are channeling these traditions and supporting the hardworking artisans who sustain them. Nope, they most definitely are not. Jason Horn has been writing about food, drinks, travel and cannabis for more than 15 years. Four different kinds of cryptocurrencies you should know. What does it mean if you smell like bread? Irreversible harm can occur when an engine overheats, and your engine may need expensive restorative repairs. Adjust accordingly. Get our latest update, offer and many more.. What is the difference between corn syrup and maple syrup? The cookie is set by the GDPR Cookie Consent plugin and is used to store whether or not user has consented to the use of cookies. Editorial team. (The disease is typically diagnosed in infants whose parents smell, well, maple syrup urine, and it can be fatal but it's fairly easily treated by regulating amino acids in the diet.). Well, we arent really sure if being maple-scented is an alcohol induced problem but In fact its not similar to Maple Syrup smelling skunk scent & their varieties. At one Toronto restaurant, he was in charge of making house-cured salmon for brunch and experimented with lots of different ingredients. Nope, it expires in 2 months. The brown color develops during boiling, as the sugars caramelize and chemically change, leading to a deeper, duskier flavor. "People started asking, What is different about this? But nobody could pick out why. What is wrong with reporter Susan Raff's arm on WFSB news? We are no longer supporting IE (Internet Explorer) as we strive to provide site experiences for browsers that support new web standards and security practices. In fact, some BA staffers prefer their waffles on the salty said. Fenugreek is an herb similar to clover that is native to the Mediterranean region, southern Europe, and western Asia. This is because you can find great maple syrups at accessible prices. Its rare but a serious metabolic disorder affecting enzyme processing abilities & potential damage to neurological development if untreated. Additionally, Some physicians recommend a trial of thiamine therapy to determine whether an affected individual is thiamine-responsive. The urine of people with this condition can smell like maple syrup. Philadelphia, PA: Elsevier; 2018:chap 22.

Cozumel Royal Caribbean Excursions, Articles W